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Natural History in Children up to 10 Years With Moderate to Profound Hearing Loss Due to Mutations in GJB2 / OTOF Genes — Otoconex  

Sensorineural Hearing Loss, Bilateral Clinical Trial

Official title:
Longitudinal Study of the Natural History of Two Autosomal Recessive Non Syndromic Deafness (DFNB1A and DFNB9) in Children up to 10 Years of Age

Clinical Trial Summary

The purpose of this study is to follow the natural history of non-syndromic hearing loss caused by mutations in two genes (GJB2 or OTOF) in children up to 10 years of age.

Clinical Trial Description

The study aims to: - better describe the prevalence of cases of DFNB1A and DFNB9, including the type of mutations, and to assess the clinical course of the disease in children up to 10 years of age who have a moderate to profound deafness. - better understand the audiological and genetic characteristics of the participants with congenital versus evolutive DFNB1A and DFNB9 deafness. ;

Study Design

Related Conditions & MeSH terms

Clinical Trial Details
NCT number NCT05402813
Study type Observational
Source Sensorion
Contact Judith LAREDO, PhD
Phone +33(0)663737108
Email judith.laredo@sensorion-pharma.com
Status Recruiting
Phase
Start date November 18, 2022
Completion date November 18, 2026
View Details
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